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二尖瓣副瓣致左室流出道隐匿性梗阻的病例报告一例及文献复习
作者:侯晓慧1  程月红1  张平洋2 
单位:1. 南京医科大学第四附属医院 超声医学科, 江苏 南京 210031;
2. 南京医科大学附属南京医院/南京市第一医院 心血管超声科, 江苏 南京 210006
关键词:心脏疾病 二尖瓣副瓣 左室流出道梗阻 罕见心脏畸形 
分类号:R445.1
出版年·卷·期(页码):2024·52·第三期(466-469)
摘要:

本文讨论罕见的心脏疾病病例,患者因持续1个月以上的反复发热及伴随头晕、乏力等症状入院就诊。其病史中包括晕厥事件、高血压病以及运动后晕倒的频繁发生。通过一系列的临床检查和影像学检查,包括心脏超声、胸部CT以及血液和骨髓培养,患者最终确诊为二尖瓣副瓣(AMVT)伴隐匿性左室流出道梗阻(LVOTO)。该病例的独特之处在于患者的症状与AMVT的静息状态下无关,而是在运动后才出现,这对于及时明确诊断和治疗提出了挑战。通过手术干预,患者得到了有效治疗,且术后随访结果正常。这个案例强调了在面对不明原因晕厥的患者时,应充分结合病史和运动激发的超声心动图检查,以明确是否存在隐匿性LVOTO,有助于准确评估病情并制定正确的诊断和治疗方案。此外,还需要注意与感染性心内膜炎和其他心脏疾病进行鉴别诊断,以排除其他可能性。

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